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summary/abstract
Amyloidosis (ICD-10: E85.9) is a heterogeneous group of misfolded protein deposition diseases; main types are AL (light-chain), ATTR (transthyretin), and AA (secondary). Diagnosis requires Congo red positivity on abdominal fat or organ biopsy with mass spectrometry typing. Per ISA 2024 and ESC Cardiac Amyloidosis 2024, AL is treated with daratumumab-VCD; ATTR uses tafamidis or patisiran/inotersen. Turkey's SUT 2025/33075 reimburses tafamidis and patisiran with cardiology/hematology board approval.